Rate-limiting enzymes of major pathways

 

Rate-Limiting Enzymes of Major Metabolic Pathways

Metabolic Pathway Rate-Limiting Enzyme
Glycolysis Phosphofructokinase-1 (PFK-1)
Gluconeogenesis Fructose-1,6-Bisphosphatase
TCA Cycle Isocitrate Dehydrogenase
Glycogenesis Glycogen Synthase
Glycogenolysis Glycogen Phosphorylase
HMP Shunt (PPP) Glucose-6-Phosphate Dehydrogenase (G6PD)
Fatty Acid Synthesis Acetyl-CoA Carboxylase (ACC)
Fatty Acid Oxidation (β-Oxidation) Carnitine Acyltransferase I (CAT-1 / CPT-1)
Cholesterol Synthesis HMG-CoA Reductase
Ketogenesis HMG-CoA Synthase (Mitochondrial)
Urea Cycle Carbamoyl Phosphate Synthetase I (CPS-I)
Heme Synthesis δ-Aminolevulinic Acid (ALA) Synthase
Purine De Novo Synthesis PRPP Amidotransferase
Pyrimidine De Novo Synthesis Carbamoyl Phosphate Synthetase II (CPS-II)