Pigmentary Disorders

 

Pigmentary Disorders

Pigmentary disorders result from either an overproduction, underproduction, or irregular distribution of melanin in the skin.

Key Classifications

Disorder Pathophysiology Clinical Presentation
Vitiligo Autoimmune destruction of melanocytes Well-circumscribed, depigmented (white) macules/patches.
Melasma Hormonal + UV-induced hypermelanosis Symmetric hyperpigmented patches on the face (cheeks, forehead).
Café-au-lait Increased melanin in epidermal keratinocytes Light-brown, oval macules; >6 suggests Neurofibromatosis type 1.

Diagnostic Pearls

  • Wood’s Lamp Examination:
    • Vitiligo: Appears as bright, chalky white patches (accentuated contrast).
    • Epidermal Pigment (Melasma): Becomes more distinct/darker.
    • Dermal Pigment: Does not change significantly in intensity.
  • Post-Inflammatory Hyperpigmentation (PIH): Common sequela of acne or inflammatory dermatoses, especially in darker skin types (Fitzpatrick IV-VI).
High-Yield Exam Pearl:

  • Vitiligo Associations: Frequently linked to other autoimmune conditions, most notably Thyroid disease (Hashimoto’s/Graves), Pernicious anemia, and Type 1 DM.
  • Café-au-lait Spots: If you see more than 6, you must think of Neurofibromatosis type 1.