Cyanotic Congenital Heart disease

 

Cyanotic Congenital Heart Disease (R-L Shunt)

Cyanotic heart defects occur when deoxygenated blood bypasses the lungs and enters the systemic circulation, leading to clinical cyanosis (hypoxemia).


1. The “5 Ts” of Cyanotic Heart Disease

  • Tetralogy of Fallot (TOF): Most common cyanotic CHD.
  • Transposition of the Great Arteries (TGA): Most common cause of cyanosis in the neonatal period.
  • Truncus Arteriosus: A single large vessel arising from both ventricles.
  • Tricuspid Atresia: Hypoplastic right ventricle.
  • Total Anomalous Pulmonary Venous Return (TAPVR): Pulmonary veins drain into the right atrium.

2. Tetralogy of Fallot (TOF) – High-Yield Details

Feature Description
Components VSD, Overriding Aorta, Pulmonary Stenosis, RV Hypertrophy.
Classic Sign “Boot-shaped heart” on chest X-ray.
“Tet” Spells Hypercyanotic episodes triggered by agitation/crying.

3. Clinical Management

  • Tet Spells: Immediate knee-chest position (increases systemic vascular resistance), supplemental O2, and morphine to reduce infundibular spasm.
  • Prostaglandin E1: Essential for ductal-dependent lesions (e.g., severe TGA, Tricuspid Atresia) to maintain systemic perfusion until surgery.

NEET PG Hint: Remember: The knee-chest position in a Tet spell works by increasing systemic vascular resistance, which decreases the right-to-left shunt across the VSD, thereby increasing pulmonary blood flow. For more high-yield pediatric cardiology and free medical questions, visit mymedschool.org.