Glucagonoma

 

Glucagonoma

A rare neuroendocrine tumor of the pancreatic alpha cells that secretes excess glucagon. It leads to a distinct constellation of symptoms, most notably a pathognomonic skin rash.

The “4 Ds” of Glucagonoma

  • Dermatitis (Necrolytic Migratory Erythema): The hallmark skin lesion.
  • Diabetes: Mild to moderate hyperglycemia due to glucagon-induced glycogenolysis and gluconeogenesis.
  • Deep Venous Thrombosis (DVT): Increased risk of thromboembolism.
  • Depression/Weight Loss: Systemic symptoms common in chronic malignancy.

Necrolytic Migratory Erythema (NME)

Feature Description
Morphology Erythematous, scaly plaques with central clearing and crusting/blistering.
Distribution Perioral, perineal, and intertriginous areas.
High-Yield Exam Pearl:

  • Diagnosis: Confirmed by markedly elevated plasma glucagon levels.
  • Association: Always consider neuroendocrine tumors in patients presenting with new-onset diabetes and a strange, migrating, erythematous rash.