Congenital anomalies of the GIT

 

Congenital GIT Anomalies

Gastrointestinal tract anomalies often stem from errors in recanalization, migration of neural crest cells, or closure of embryonic structures.

Anomaly Pathophysiology / Presentation
Esophageal Atresia/Fistula Failure of the tracheoesophageal septum to divide. Presents with polyhydramnios, drooling, and choking/cyanosis on feeding.
Hypertrophic Pyloric Stenosis Hypertrophy of pyloric smooth muscle. Presents with “olive-sized” mass and non-bilious, projectile vomiting in infants.
Hirschsprung Disease Failure of neural crest cells to migrate. Leads to the aganglionic distal colon (Auerbach/Meissner plexus). Bilious vomiting, failure to pass meconium.
Meckel Diverticulum Persistence of the vitelline duct. Can contain ectopic gastric/pancreatic tissue. Follows “Rule of 2s.”
High-Yield Clinical Pearls:

  • Bilious vs. Non-bilious: Vomiting distal to the Ampulla of Vater is usually bilious. Pyloric stenosis is proximal, hence non-bilious.
  • Malrotation: Often leads to midgut volvulus; look for “Ladd’s bands” compressing the duodenum.